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Orofacial Pain as the Sole Manifestation of Syringobulbia-Syringomyelia Associated with Arnold-Chiari Malformation
1Valencia University Medical and Dental School, Valencia, Spain
2Orofacial Pain Center, University of Kentucky, Lexington, Kentucky
3General University Hospital, Valencia, Spain
*Corresponding Author(s): Miguel Peñarrocha E-mail: penarroc@uv.es
This is a case report of a male patient who presented with orofacial pain for a year as the only manifestation of syringobulbia-syringomyelia associated with Arnold-Chiari malformation. This article places emphasis on the clinical presentation and possible differential diagnoses. The pain was continuous and affected the left side of the face. It was exacerbated by coughing and physical effort, possibly as a consequence of an increase in intracranial pressure. Paroxysmal pain crises developed over this background of continuous pain, compatible with neurogenic trigeminal pain of the left second branch, together with pain episodes similar to cluster headache on the same side. The symptoms were resolved following neurosurgical management with amplification of the foramen magnum.
orofacial pain; syringobulbia-syringomyelia; Arnold-Chiari malformation
Miguel Peñarrocha,Jeffrey P. Okeson,Maria S. Peñarrocha,M. Angeles Cervelló. Orofacial Pain as the Sole Manifestation of Syringobulbia-Syringomyelia Associated with Arnold-Chiari Malformation. Journal of Oral & Facial Pain and Headache. 2001. 15(2);170-173.
1. Mancall EL. Syringomyelia. In: Rowland LP (ed). Merritt’s Textbook of Neurology, ed 8. Philadelphia: Lea & Febiger, 1989:687–691.
2. Greer M. Arnold-Chiari malformation. In: Rowland LP (ed). Merritt’s Textbook of Neurology, ed 8. Philadelphia: Lea & Febiger, 1989:480–483.
3. Pearce JM. Cervicogenic headache. A personal view. Cephalalgia 1995;15:463–469.
4. Laplane D. Siringomielia. In: Lhermitte F, Mamo H (eds). Los sistemas nervioso y muscular. Paris: Expaxs, 1973:217–220.
5. Sayette V, Leproux F, Letellier P. Cervical cord and dorsal medullary infarction presenting with retro-orbital pain. Neurology 1999;53:632–634.
6. Sayette V, Schaeffer S, Coskun O, Leproux F, Defer G. Cluster headache-like attack as an opening symptom of a unilateral infarction of the cervical cord. Persistent anaesthesia and dysaesthesia to cold stimuli. J Neurol Neurosurg Psych 1999;66:397–400.
7. Lazhortes G. Nervio trigémino. In: Lazorthes G (ed). Sistema nervioso periférico. Barcelona: Toray-Masson, 1976:61–91.
8. Gambardella G, Caruso G, Caffo M, Germano A, La Rosa G, Tomasello F. Transverse microincisions of the outer layer of the dura mater combined with foramen magnum decompression as treatment for syringomyelia with Chiari I malformation. Acta Neurochirurgica 1998;140:134–139.
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